SCOLIOSIS
Definition:
Curvature of the spine.
Author’s Comment: This condition needs to be followed closely by your child’s doctor or at a recommended orthopedic facility. Most children end up needing no treatment, but occasionally the condi- tion will progress to the point where more aggressive therapy is needed.
1. What causes this condition to occur in my child? Scoliosis occurs at different ages and for different potential reasons. The common version of scoliosis is the type that occurs in preadoles- cence to adolescence, mainly in girls, and has no currently known cause. There is a genetic component of scoliosis, but there is no iden- tifiable gene or genetic test to determine if one is at risk for devel- oping scoliosis, other than family history.
Other children with scoliosis are born with abnormalities of the spine, but this is very uncommon. Some children will develop scol- iosis due to an abnormality of the spine development; this is also unusual as well, but it is looked for during the examination of the child. Other conditions that can cause scoliosis are underlying imbal- ances in the nervous or musculature system.
2. Is it hereditary?
The type of scoliosis that occurs in preadolescence and adolescence can be hereditary. If the family history is positive for scoliosis, the children should be screened. Other disorders that can cause scoliosis are abnor- malities of the spinal cord or brain and are not typically hereditary.
3. What is the natural progression of this disorder?
The natural progression is unpredictable. Some people have scoliosis that never changes, some have scoliosis that progresses a little bit and then becomes static, some people have scoliosis that progresses and requires treatment. Once a curve starts to develop, it can progress at a rate of one degree every month. So, over the course of an entire year, a curve can progress twelve degrees. Rarely can it progress more; it is a very variable condition. An important feature is that it can progress while the child is still growing.
Once the child has completed growth and the skeleton is mature, as long as the curve is less than forty degrees, it will not progress as an adult. If the curve is greater than forty degrees, there is a steadily increasing risk that the curve will progress, even after the child has completed growth. The size of the curve at the end of growth is an important feature to note because this determines the lifetime risk of progression.
4. What symptoms can occur because of this condition? Most scoliosis is completely asymptomatic and causes no pain or discomfort at all in the early stage. Since there are no early symp- toms, the early diagnosis of scoliosis is made with screening.
Scoliosis is common enough now that school nurses screen for this, as well as the pediatrician upon a wellness examination at the age of six years and beyond.
Symptoms can occur because of scoliosis, the most common being the child holding one shoulder higher than the other or sometimes having a feeling of imbalance. Once the curve becomes larger than forty degrees, back pain can start to occur. When the spine curves to this degree, it puts abnormal forces on the joints of the back that can cause pain. Sometimes the ribs will literally bend over and touch the pelvic bone, which can cause discomfort. Curves that progress beyond sixty degrees can start to cause measurable changes in lung function. Curves that progress beyond eighty degrees can cause changes in heart function and become life threatening.
5. How will this condition limit my child’s participation in athletics?
Scoliosis itself does not interfere with activities. Children or adults who have scoliosis can be active and do any activity. In fact, there are good reasons to be physically active to keep your child’s muscles in balance and his or her posture well aligned. To that end, physical activity is encouraged. Participation in athletics is not limited by having scoliosis.
6. What is the treatment for this disorder?
The treatment depends on the degree of the curvature. Curves that are less than twenty degrees are just observed and checked periodi- cally with repeat physical examinations and X rays. If the curve of the spine becomes larger than twenty degrees, the degree of maturity of the spine and pelvis are used to judge the risk or further progression.
Based on this knowledge, a decision for bracing may be recommended. In children who have a lot of growth remaining whose curves are larger than twenty degrees, bracing may well be recommended.
There are two options for bracing, either full time or nighttime. The Boston brace is the full-time brace, also referred to as TLSO. The Boston brace is considered full-time bracing and needs to be worn for at least eighteen hours a day. With some curves that affect only the lower back, there is an option for wearing a nighttime brace known as a Charleston brace; this is worn only during sleeping. There are only a few curves where this brace can be used.
Physical therapy has not been objectively shown to improve the condition, but it certainly helps from a sense of well-being and overall good health. I believe it is important to learn good back mechanics and posture. A short course of physical therapy to teach these behaviors is helpful. Along the same line, other activities that help teach posture, balance, and form, such as dance or martial arts, can also be helpful.
The next level of treatment is surgery. Surgery is reserved for chil- dren whose curves are progressing despite the use of a brace and whose curves are larger than forty degrees. The main reason for recom- mending scoliosis surgery is that curves that are larger than forty degrees are likely to continue to increase as time passes. In many respects the sooner that scoliosis surgery is accomplished to straighten the spine and keep it from curving, the easier it is technically to do the surgery. The surgery itself has a fairly lengthy recovery time; it takes almost three months to recover from having the spine straight- ened and fused. Scoliosis surgery can be done into the adult years, but with age, the spine is stiffer and the potential for difficulties and complications is greater.
The surgery itself involves straightening the spine and holding the spine straight with a series of metal rods placed into the spine to keep it straight while the bone fuses. The tradeoff is that it takes the spine that is flexible and curved and changes it to a spine that is straight, fused, and stiff. The decision to proceed with surgery does not need to be rushed. There is plenty of time to seek a second or third opinion. This is a major, potentially life-threatening surgery that involves a lot of blood loss and a long period of recovery. On average, it takes most people six weeks from the surgery date to feel comfortable again and almost three months to regain energy.
7. How often will X rays be required to follow its progress?
This depends on the age of the person upon diagnosis, the maturity of the spine, and the degree of curve. Since the fastest rate of progression of a curve is roughly one degree per month, most orthopedists will perform X rays every six months to follow curve progression. If rapid curve progression is suspected, the X rays can be requested every four months. Since X rays involve radiation, it is important to try and keep the X rays to those that are needed and not more.
Upon the initial diagnosis, it is important to get an X ray of the spine looking at it from the front and side. To just follow the scoliosis itself, a front view X ray only is needed; this cuts the radiation dose in half. Doing another X ray to take a look at the spine from the side really only needs to be done again if surgery is being contemplated for a final picture of the spine. X rays can be done to show the spine with shielding of important organs. In young females, the breasts can be shielded with special lead aprons. The gonads in males can also be shielded. If the X ray technician does not offer to do this, it is important to request this shielding.
8. Are there any exercises that can be performed to strengthen the back and to slow down the progression of this condition?
There are no studies on the value of exercise in slowing down scol- iosis. Regardless of the condition, it is important to learn good back posture, training, and mechanics. To this end, seeing a physical ther- apist for some back exercises is useful. Other activities that are useful for controlling the back and helping alignment are yoga, dance, and martial arts.
9. What role does surgery play in the correction of this disorder?
Surgery plays the ultimate role in straightening the spine once the spine has curved more than forty degrees. Surgery straightens the spine and removes the curve. To keep the curve from coming back, the spine is straightened, metal rods are inserted, and the spine is fused. As a result, the spine is taken from a flexible curve to a rigid, straight spine. The results of spine surgery can result in mechanical problems of the back decades later. Further back surgery may be required.
10. Do we need to be referred to a doctor or institution that specializes in this condition?
Like any medical condition, one should see a physician and/or institu- tion trained to take care of that particular disorder. Pediatric orthope- dists are trained to take care of scoliosis. Only a small percentage of adult spine surgeons perform scoliosis surgery, and they treat the patients as adults, not young, growing people. There are some centers that specialize in scoliosis surgery only and some that treat a variety of orthopedic issues. If you have any questions regarding the physician’s training or experience, please ask. The Internet is very useful tool in this regard as well.
11. What kind of follow-up will be needed in the future?
The follow-up depends on the age of your child, the size of the curve, and the potential for curve progression. In general, scoliosis is followed until (1) the child completes growth and the curve does not require treatment or (2) the child continues to grow and the curve grows to the point of requiring treatment. Once the child’s spine has completed growth, no further follow-up studies are needed. If scoliosis reaches the point of requiring surgery, once the spine has been fused there is a one-year follow-up. If there have been no complications after one year, no further follow-up is needed.
W. BARRY HUMENIUK, MD
Orthopedics